| Identification | Back Directory | [Name]
N-ISOVALEROYLGLYCINE | [CAS]
16284-60-9 | [Synonyms]
Isovalerylglycine
Isovaleroylglycine
N-ISOVALERYLGLYCINE
N-ISOVALEROYLGLYCINE
N-Isovalerylglycine-d2
2-(3-Methylbutanamido)
N-ISOVALEROYLGLYCINE 98+%
N-(3-Methylbutyryl)glycine
N-(3-Methyl-1-oxobutyl)glycine
2-(3-MethylbutanaMido)acetic acid
(3-methyl-butyrylamino)-acetic acid | [Molecular Formula]
C7H13NO3 | [MDL Number]
MFCD00059629 | [MOL File]
16284-60-9.mol | [Molecular Weight]
159.18 |
| Chemical Properties | Back Directory | [Melting point ]
105°C | [Boiling point ]
371.8±25.0 °C(Predicted) | [density ]
1.097±0.06 g/cm3(Predicted) | [storage temp. ]
Sealed in dry,Room Temperature | [solubility ]
DMSO (Slightly), Methanol (Slightly) | [form ]
Solid | [pka]
3.58±0.10(Predicted) | [color ]
White to Off-White | [BRN ]
1766622 |
| Hazard Information | Back Directory | [Chemical Properties]
White to Off-White Solid | [Uses]
N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with
isovaleric acidemia, an inborn error of leucine metabolism. | [Definition]
ChEBI: An N-acylglycine in which the acyl group is specified as isovaleryl. | [Description]
Isovaleroylglycine is a compound found in the urine of patients with isovaleric acidemia, a disorder created by defective leucine metabolism due to a deficiency in the isovaleryl coenzyme A dehydrogenase.1 It has been used as a diagnostic tool in the diagnosis of various acidemias and mitochondrial fatty acid β-oxidation defects. |
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